COVID19 ICD10CM Value Set for Inborn Errors of Metabolism

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          "valueInteger" : 227
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  "date" : "2023-06-21T18:16:37-04:00",
  "meta" : {
    "versionId" : "13",
    "lastUpdated" : "2022-07-14T01:03:32.000-04:00",
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  "purpose" : "(Clinical Focus: This set of values contains terms related to inborn errors of metabolism and is listed as a chronic metabolic disease on the CDC SARS-CoV-2 hospitalization surveillance case report form.),(Data Element Scope: ),(Inclusion Criteria: Includes inborn errors of metabolism such as Acyl-CoA oxidase deficiency, Alpha-1-antitrypsin deficiency, Crigler-Najjar syndrome, glycogen storage diseases, mucopolysaccharidosis, Niemann-Pick disease, pyruvate carboxylase deficiency and Tay-Sachs disease.),(Exclusion Criteria: )",
  "name" : "COVID19ICD10CMValueSetForInbornErrorsOfMetabolism",
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  "expansion" : {
    "contains" : [ {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70",
      "display" : "Disorders of aromatic amino-acid metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.0",
      "display" : "Classical phenylketonuria",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.1",
      "display" : "Other hyperphenylalaninemias",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.2",
      "display" : "Disorders of tyrosine metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.20",
      "display" : "Disorder of tyrosine metabolism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.21",
      "display" : "Tyrosinemia",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.29",
      "display" : "Other disorders of tyrosine metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.3",
      "display" : "Albinism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.30",
      "display" : "Albinism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.31",
      "display" : "Ocular albinism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.310",
      "display" : "X-linked ocular albinism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.311",
      "display" : "Autosomal recessive ocular albinism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.318",
      "display" : "Other ocular albinism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.319",
      "display" : "Ocular albinism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.32",
      "display" : "Oculocutaneous albinism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.320",
      "display" : "Tyrosinase negative oculocutaneous albinism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.321",
      "display" : "Tyrosinase positive oculocutaneous albinism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.328",
      "display" : "Other oculocutaneous albinism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.329",
      "display" : "Oculocutaneous albinism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.33",
      "display" : "Albinism with hematologic abnormality",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.330",
      "display" : "Chediak-Higashi syndrome",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.331",
      "display" : "Hermansky-Pudlak syndrome",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.338",
      "display" : "Other albinism with hematologic abnormality",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.339",
      "display" : "Albinism with hematologic abnormality, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.39",
      "display" : "Other specified albinism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.4",
      "display" : "Disorders of histidine metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.40",
      "display" : "Disorders of histidine metabolism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.41",
      "display" : "Histidinemia",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.49",
      "display" : "Other disorders of histidine metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.5",
      "display" : "Disorders of tryptophan metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.8",
      "display" : "Other disorders of aromatic amino-acid metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.81",
      "display" : "Aromatic L-amino acid decarboxylase deficiency",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.89",
      "display" : "Other disorders of aromatic amino-acid metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E70.9",
      "display" : "Disorder of aromatic amino-acid metabolism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71",
      "display" : "Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.0",
      "display" : "Maple-syrup-urine disease",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.1",
      "display" : "Other disorders of branched-chain amino-acid metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.11",
      "display" : "Branched-chain organic acidurias",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.110",
      "display" : "Isovaleric acidemia",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.111",
      "display" : "3-methylglutaconic aciduria",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.118",
      "display" : "Other branched-chain organic acidurias",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.12",
      "display" : "Disorders of propionate metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.120",
      "display" : "Methylmalonic acidemia",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.121",
      "display" : "Propionic acidemia",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.128",
      "display" : "Other disorders of propionate metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.19",
      "display" : "Other disorders of branched-chain amino-acid metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.2",
      "display" : "Disorder of branched-chain amino-acid metabolism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.3",
      "display" : "Disorders of fatty-acid metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.30",
      "display" : "Disorder of fatty-acid metabolism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.31",
      "display" : "Disorders of fatty-acid oxidation",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.310",
      "display" : "Long chain/very long chain acyl CoA dehydrogenase deficiency",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.311",
      "display" : "Medium chain acyl CoA dehydrogenase deficiency",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.312",
      "display" : "Short chain acyl CoA dehydrogenase deficiency",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.313",
      "display" : "Glutaric aciduria type II",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.314",
      "display" : "Muscle carnitine palmitoyltransferase deficiency",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.318",
      "display" : "Other disorders of fatty-acid oxidation",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.32",
      "display" : "Disorders of ketone metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.39",
      "display" : "Other disorders of fatty-acid metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.4",
      "display" : "Disorders of carnitine metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.40",
      "display" : "Disorder of carnitine metabolism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.41",
      "display" : "Primary carnitine deficiency",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.42",
      "display" : "Carnitine deficiency due to inborn errors of metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.43",
      "display" : "Iatrogenic carnitine deficiency",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.44",
      "display" : "Other secondary carnitine deficiency",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.440",
      "display" : "Ruvalcaba-Myhre-Smith syndrome",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.448",
      "display" : "Other secondary carnitine deficiency",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.5",
      "display" : "Peroxisomal disorders",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.50",
      "display" : "Peroxisomal disorder, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.51",
      "display" : "Disorders of peroxisome biogenesis",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.510",
      "display" : "Zellweger syndrome",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.511",
      "display" : "Neonatal adrenoleukodystrophy",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.518",
      "display" : "Other disorders of peroxisome biogenesis",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.52",
      "display" : "X-linked adrenoleukodystrophy",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.520",
      "display" : "Childhood cerebral X-linked adrenoleukodystrophy",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.521",
      "display" : "Adolescent X-linked adrenoleukodystrophy",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.522",
      "display" : "Adrenomyeloneuropathy",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.528",
      "display" : "Other X-linked adrenoleukodystrophy",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.529",
      "display" : "X-linked adrenoleukodystrophy, unspecified type",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.53",
      "display" : "Other group 2 peroxisomal disorders",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.54",
      "display" : "Other peroxisomal disorders",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.540",
      "display" : "Rhizomelic chondrodysplasia punctata",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.541",
      "display" : "Zellweger-like syndrome",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.542",
      "display" : "Other group 3 peroxisomal disorders",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E71.548",
      "display" : "Other peroxisomal disorders",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72",
      "display" : "Other disorders of amino-acid metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.0",
      "display" : "Disorders of amino-acid transport",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.00",
      "display" : "Disorders of amino-acid transport, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.01",
      "display" : "Cystinuria",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.02",
      "display" : "Hartnup's disease",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.03",
      "display" : "Lowe's syndrome",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.04",
      "display" : "Cystinosis",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.09",
      "display" : "Other disorders of amino-acid transport",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.1",
      "display" : "Disorders of sulfur-bearing amino-acid metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.10",
      "display" : "Disorders of sulfur-bearing amino-acid metabolism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.11",
      "display" : "Homocystinuria",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.12",
      "display" : "Methylenetetrahydrofolate reductase deficiency",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.19",
      "display" : "Other disorders of sulfur-bearing amino-acid metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.2",
      "display" : "Disorders of urea cycle metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.20",
      "display" : "Disorder of urea cycle metabolism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.21",
      "display" : "Argininemia",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.22",
      "display" : "Arginosuccinic aciduria",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.23",
      "display" : "Citrullinemia",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.29",
      "display" : "Other disorders of urea cycle metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.3",
      "display" : "Disorders of lysine and hydroxylysine metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.4",
      "display" : "Disorders of ornithine metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.5",
      "display" : "Disorders of glycine metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.50",
      "display" : "Disorder of glycine metabolism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.51",
      "display" : "Non-ketotic hyperglycinemia",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.52",
      "display" : "Trimethylaminuria",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.53",
      "display" : "Primary hyperoxaluria",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.59",
      "display" : "Other disorders of glycine metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.8",
      "display" : "Other specified disorders of amino-acid metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.81",
      "display" : "Disorders of gamma aminobutyric acid metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.89",
      "display" : "Other specified disorders of amino-acid metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E72.9",
      "display" : "Disorder of amino-acid metabolism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74",
      "display" : "Other disorders of carbohydrate metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.0",
      "display" : "Glycogen storage disease",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.00",
      "display" : "Glycogen storage disease, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.01",
      "display" : "von Gierke disease",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.02",
      "display" : "Pompe disease",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.03",
      "display" : "Cori disease",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.04",
      "display" : "McArdle disease",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.09",
      "display" : "Other glycogen storage disease",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.1",
      "display" : "Disorders of fructose metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.10",
      "display" : "Disorder of fructose metabolism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.11",
      "display" : "Essential fructosuria",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.12",
      "display" : "Hereditary fructose intolerance",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.19",
      "display" : "Other disorders of fructose metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.2",
      "display" : "Disorders of galactose metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.20",
      "display" : "Disorders of galactose metabolism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.21",
      "display" : "Galactosemia",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.29",
      "display" : "Other disorders of galactose metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.3",
      "display" : "Other disorders of intestinal carbohydrate absorption",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.31",
      "display" : "Sucrase-isomaltase deficiency",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.39",
      "display" : "Other disorders of intestinal carbohydrate absorption",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.4",
      "display" : "Disorders of pyruvate metabolism and gluconeogenesis",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.8",
      "display" : "Other specified disorders of carbohydrate metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.81",
      "display" : "Disorders of glucose transport, not elsewhere classified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.810",
      "display" : "Glucose transporter protein type 1 deficiency",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.818",
      "display" : "Other disorders of glucose transport",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.819",
      "display" : "Disorders of glucose transport, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.89",
      "display" : "Other specified disorders of carbohydrate metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E74.9",
      "display" : "Disorder of carbohydrate metabolism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75",
      "display" : "Disorders of sphingolipid metabolism and other lipid storage disorders",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.0",
      "display" : "GM2 gangliosidosis",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.00",
      "display" : "GM2 gangliosidosis, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.01",
      "display" : "Sandhoff disease",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.02",
      "display" : "Tay-Sachs disease",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.09",
      "display" : "Other GM2 gangliosidosis",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.1",
      "display" : "Other and unspecified gangliosidosis",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.10",
      "display" : "Unspecified gangliosidosis",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.11",
      "display" : "Mucolipidosis IV",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.19",
      "display" : "Other gangliosidosis",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.2",
      "display" : "Other sphingolipidosis",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.21",
      "display" : "Fabry (-Anderson) disease",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.22",
      "display" : "Gaucher disease",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.23",
      "display" : "Krabbe disease",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.24",
      "display" : "Niemann-Pick disease",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.240",
      "display" : "Niemann-Pick disease type A",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.241",
      "display" : "Niemann-Pick disease type B",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.242",
      "display" : "Niemann-Pick disease type C",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.243",
      "display" : "Niemann-Pick disease type D",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.244",
      "display" : "Niemann-Pick disease type A/B",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.248",
      "display" : "Other Niemann-Pick disease",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.249",
      "display" : "Niemann-Pick disease, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.25",
      "display" : "Metachromatic leukodystrophy",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.26",
      "display" : "Sulfatase deficiency",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.29",
      "display" : "Other sphingolipidosis",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.3",
      "display" : "Sphingolipidosis, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.4",
      "display" : "Neuronal ceroid lipofuscinosis",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.5",
      "display" : "Other lipid storage disorders",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E75.6",
      "display" : "Lipid storage disorder, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E76",
      "display" : "Disorders of glycosaminoglycan metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E76.0",
      "display" : "Mucopolysaccharidosis, type I",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E76.01",
      "display" : "Hurler's syndrome",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E76.02",
      "display" : "Hurler-Scheie syndrome",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E76.03",
      "display" : "Scheie's syndrome",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E76.1",
      "display" : "Mucopolysaccharidosis, type II",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E76.2",
      "display" : "Other mucopolysaccharidoses",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E76.21",
      "display" : "Morquio mucopolysaccharidoses",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E76.210",
      "display" : "Morquio A mucopolysaccharidoses",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E76.211",
      "display" : "Morquio B mucopolysaccharidoses",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E76.219",
      "display" : "Morquio mucopolysaccharidoses, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E76.22",
      "display" : "Sanfilippo mucopolysaccharidoses",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E76.29",
      "display" : "Other mucopolysaccharidoses",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E76.3",
      "display" : "Mucopolysaccharidosis, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E76.8",
      "display" : "Other disorders of glucosaminoglycan metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E76.9",
      "display" : "Glucosaminoglycan metabolism disorder, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78",
      "display" : "Disorders of lipoprotein metabolism and other lipidemias",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.0",
      "display" : "Pure hypercholesterolemia",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.00",
      "display" : "Pure hypercholesterolemia, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.01",
      "display" : "Familial hypercholesterolemia",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.1",
      "display" : "Pure hyperglyceridemia",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.2",
      "display" : "Mixed hyperlipidemia",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.3",
      "display" : "Hyperchylomicronemia",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.4",
      "display" : "Other hyperlipidemia",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.41",
      "display" : "Elevated Lipoprotein(a)",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.49",
      "display" : "Other hyperlipidemia",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.5",
      "display" : "Hyperlipidemia, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.6",
      "display" : "Lipoprotein deficiency",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.7",
      "display" : "Disorders of bile acid and cholesterol metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.70",
      "display" : "Disorder of bile acid and cholesterol metabolism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.71",
      "display" : "Barth syndrome",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.72",
      "display" : "Smith-Lemli-Opitz syndrome",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.79",
      "display" : "Other disorders of bile acid and cholesterol metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.8",
      "display" : "Other disorders of lipoprotein metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.81",
      "display" : "Lipoid dermatoarthritis",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.89",
      "display" : "Other lipoprotein metabolism disorders",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E78.9",
      "display" : "Disorder of lipoprotein metabolism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E79",
      "display" : "Disorders of purine and pyrimidine metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E79.0",
      "display" : "Hyperuricemia without signs of inflammatory arthritis and tophaceous disease",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E79.1",
      "display" : "Lesch-Nyhan syndrome",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E79.2",
      "display" : "Myoadenylate deaminase deficiency",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E79.8",
      "display" : "Other disorders of purine and pyrimidine metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E79.9",
      "display" : "Disorder of purine and pyrimidine metabolism, unspecified",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E80",
      "display" : "Disorders of porphyrin and bilirubin metabolism",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E80.0",
      "display" : "Hereditary erythropoietic porphyria",
      "version" : "2023"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "E80.1",
      "display" : "Porphyria cutanea tarda",
      "version" : "2023"
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