Disorders of the Immune System

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  "date" : "2024-02-06T01:09:28-05:00",
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  "purpose" : "(Clinical Focus: The purpose of this value set is to represent concepts for a diagnosis of conditions affecting the immune system.),(Data Element Scope: This value set may use a model element related to Diagnosis.),(Inclusion Criteria: Includes concepts that represent a diagnosis of disorders of the immune system including disorders of the immunoglobulins and the complement system.),(Exclusion Criteria: No exclusions.)",
  "name" : "DisordersOfTheImmuneSystem",
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      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D80.0",
      "display" : "Hereditary hypogammaglobulinemia",
      "version" : "2024"
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      "code" : "D80.1",
      "display" : "Nonfamilial hypogammaglobulinemia",
      "version" : "2024"
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      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D80.2",
      "display" : "Selective deficiency of immunoglobulin A [IgA]",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D80.3",
      "display" : "Selective deficiency of immunoglobulin G [IgG] subclasses",
      "version" : "2024"
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      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D80.4",
      "display" : "Selective deficiency of immunoglobulin M [IgM]",
      "version" : "2024"
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      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D80.5",
      "display" : "Immunodeficiency with increased immunoglobulin M [IgM]",
      "version" : "2024"
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      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D80.6",
      "display" : "Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia",
      "version" : "2024"
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      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D80.7",
      "display" : "Transient hypogammaglobulinemia of infancy",
      "version" : "2024"
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      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D80.8",
      "display" : "Other immunodeficiencies with predominantly antibody defects",
      "version" : "2024"
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      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D80.9",
      "display" : "Immunodeficiency with predominantly antibody defects, unspecified",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D81.0",
      "display" : "Severe combined immunodeficiency [SCID] with reticular dysgenesis",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D81.1",
      "display" : "Severe combined immunodeficiency [SCID] with low T- and B-cell numbers",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D81.2",
      "display" : "Severe combined immunodeficiency [SCID] with low or normal B-cell numbers",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D81.4",
      "display" : "Nezelof's syndrome",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D81.6",
      "display" : "Major histocompatibility complex class I deficiency",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D81.7",
      "display" : "Major histocompatibility complex class II deficiency",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D81.82",
      "display" : "Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D81.89",
      "display" : "Other combined immunodeficiencies",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D81.9",
      "display" : "Combined immunodeficiency, unspecified",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D82.0",
      "display" : "Wiskott-Aldrich syndrome",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D82.1",
      "display" : "Di George's syndrome",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D82.2",
      "display" : "Immunodeficiency with short-limbed stature",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D82.3",
      "display" : "Immunodeficiency following hereditary defective response to Epstein-Barr virus",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D82.4",
      "display" : "Hyperimmunoglobulin E [IgE] syndrome",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D82.8",
      "display" : "Immunodeficiency associated with other specified major defects",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D82.9",
      "display" : "Immunodeficiency associated with major defect, unspecified",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D83.0",
      "display" : "Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D83.1",
      "display" : "Common variable immunodeficiency with predominant immunoregulatory T-cell disorders",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D83.2",
      "display" : "Common variable immunodeficiency with autoantibodies to B- or T-cells",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D83.8",
      "display" : "Other common variable immunodeficiencies",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D83.9",
      "display" : "Common variable immunodeficiency, unspecified",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D84.0",
      "display" : "Lymphocyte function antigen-1 [LFA-1] defect",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D84.1",
      "display" : "Defects in the complement system",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D84.81",
      "display" : "Immunodeficiency due to conditions classified elsewhere",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D84.821",
      "display" : "Immunodeficiency due to drugs",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D84.822",
      "display" : "Immunodeficiency due to external causes",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D84.89",
      "display" : "Other immunodeficiencies",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D84.9",
      "display" : "Immunodeficiency, unspecified",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D89.3",
      "display" : "Immune reconstitution syndrome",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D89.810",
      "display" : "Acute graft-versus-host disease",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D89.811",
      "display" : "Chronic graft-versus-host disease",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D89.812",
      "display" : "Acute on chronic graft-versus-host disease",
      "version" : "2024"
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      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D89.813",
      "display" : "Graft-versus-host disease, unspecified",
      "version" : "2024"
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      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D89.82",
      "display" : "Autoimmune lymphoproliferative syndrome [ALPS]",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D89.831",
      "display" : "Cytokine release syndrome, grade 1",
      "version" : "2024"
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      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D89.832",
      "display" : "Cytokine release syndrome, grade 2",
      "version" : "2024"
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      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D89.833",
      "display" : "Cytokine release syndrome, grade 3",
      "version" : "2024"
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      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D89.834",
      "display" : "Cytokine release syndrome, grade 4",
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      "code" : "D89.835",
      "display" : "Cytokine release syndrome, grade 5",
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      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D89.839",
      "display" : "Cytokine release syndrome, grade unspecified",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D89.84",
      "display" : "IgG4-related disease",
      "version" : "2024"
    }, {
      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D89.89",
      "display" : "Other specified disorders involving the immune mechanism, not elsewhere classified",
      "version" : "2024"
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      "system" : "http://hl7.org/fhir/sid/icd-10-cm",
      "code" : "D89.9",
      "display" : "Disorder involving the immune mechanism, unspecified",
      "version" : "2024"
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    "timestamp" : "2024-04-23T18:53:16-04:00"
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  "title" : "Disorders of the Immune System",
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